Multicentric osteolysis-nodulosis-arthropathy spectrum

Orpha code: 371428OMIM code: 277950

Definition

A rare systemic or rheumatologic disease characterized by peripheral osteolysis (especially carpal and tarsal bones), interphalangeal joint erosions, subcutaneous fibrocollagenous nodules, facial dysmorphism, and a wide range of associated manifestations.

Disease data
Classification

Disease

Synonyms
MONA spectrum
Spektrum MONA
NAO syndrome
Nodulosis-arthropathy-osteolysis syndrome
Torg-Winchester syndrome
ORPHA code
371428
OMIM code
277950
ICD10 code
M89.5
ICD11 code
-

No additional description.

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