Primary non-essential cutis verticis gyrata

Orpha code: 357225OMIM code: 219300

Definicja

Primary non-essential cutis verticis gyrata is a rare, genetic, dermis disorder characterized by slowly progressive thickening of the scalp, which becomes raised and forms ridges and furrows with symmetrical distribution resembling the cerebral gyri and cannot be flattened by traction or pressure, associated with ophthalmologic (e.g. congenital cataract) and/or neurological abnormalities (e.g. intellectual disability, epilepsy, microcephaly, encephalopathy).

Disease data
Klasyfikacja

Disease

Kod ORPHA
357225
Kod OMIM
219300
Kod ICD10
Q82.8
Kod ICD11
-

No additional description.

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