Glutaric acidemia type 3

Orpha code: 35706OMIM code: 231690

Definition

A rare inborn error of metabolism characterized by abnormally high urinary excretion of glutaric acid due to peroxisomal glutaryl-CoA oxidase deficiency. There is no association with a specific clinical phenotype.

Disease data
Classification

Disease

Synonyms
Glutaric aciduria type 3
Acyduria glutarowa typu 3
Niedobór oksydazy glutarylo-CoA
Glutaryl-CoA oxidase deficiency
ORPHA code
35706
OMIM code
231690
ICD10 code
E72.3
ICD11 code
-

No additional description.

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