Galactosialidosis

Orpha code: 351OMIM code: 256540

Definition

Galactosialidosis is a lysosomal storage disease characterized by coarse facial features, macular ''cherry red spot'', and dysostosis multiplex. Clinical presentation can be heterogenous ranging from a severe, early-onset, rapidly progressive infantile form to late onset, slowly progressive juvenile/adult form.

Disease data
Classification

Disease

Synonyms
Goldberg syndrome
Niedobór neuraminidazy z niedoborem beta-galaktozydazy
Zespół Goldberga
Neuraminidase deficiency with beta-galactosidase deficiency
ORPHA code
351
OMIM code
256540
ICD10 code
E77.1
ICD11 code
5C56.21

No additional description.

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