Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Congenital factor XIII deficiency is an inherited bleeding disorder due to reduced levels and activity of factor XIII (FXIII) and characterized by hemorrhagic diathesis frequently associated with spontaneous abortions and defective wound healing. Factor XIII deficiency is one of the most rare coagulation factor deficiencies. Disease data Classification Disease Synonyms Fibrin-stabilizing factor deficiency Niedobór czynnika stabilizującego włóknik ORPHA code 331 OMIM code 613235 ICD10 code D68.2 ICD11 code 3B14.Z *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl