Congenital factor X deficiency

Orpha code: 328OMIM code: 227600

Definition

A rare inherited bleeding disorder with a decreased antigen and/or activity of factor X (FX) and characterized by mild to severe bleeding symptoms.

Disease data
Classification

Disease

Synonyms
Congenital Stuart factor deficiency
Wrodzony Niedobór czynnika Stuarta
Wrodzony Niedobór czynnika Stuarta i Prowera
Stuart-Prower factor deficiency
ORPHA code
328
OMIM code
227600
ICD10 code
D68.2
ICD11 code
3B14.1

No additional description.

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