Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Dehydrated hereditary stomatocytosis (DHS) is a rare hemolytic anemia characterized by a decreased red cell osmotic fragility due to a defect in cation permeability, resulting in red cell dehydration and mild to moderate compensated hemolysis. Pseudohyperkalemia (loss of potassium ions from red cells on storage at room temperature) is sometimes observed. Disease data Classification Disease Synonyms Hereditary xerocytosis Dziedziczna kserocytoza ORPHA code 3202 OMIM code 616689 ICD10 code D58.8 ICD11 code 3A10.Y *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl