Tubulocystic renal cell carcinoma

Orpha code: 319325OMIM code:

Definition

Tubulocystic renal cell carcinoma is an extremely rare subtype of renal cell carcinoma most frequently characterized by a small, solitary, well-circumscribed, unencapsulated renal tumor composed of multiple small to medium-sized cysts with a white or gray, spongy ("bubble wrap-like") cut surface. Patients are usually asymptomatic or could manifest with abdominal pain, abdominal distension and/or hematuria. Progression, recurrence and metastasis rarely occur although lymph node, bone, pleura and liver metastases have been reported.

Disease data
Classification

Disease

ORPHA code
319325
OMIM code
-
ICD10 code
C64
ICD11 code
-

No additional description.

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