Rak cewkowo-torbielowaty

Kod Orpha: 319325Kod OMIM:

Definicja

Tubulocystic renal cell carcinoma is an extremely rare subtype of renal cell carcinoma most frequently characterized by a small, solitary, well-circumscribed, unencapsulated renal tumor composed of multiple small to medium-sized cysts with a white or gray, spongy ("bubble wrap-like") cut surface. Patients are usually asymptomatic or could manifest with abdominal pain, abdominal distension and/or hematuria. Progression, recurrence and metastasis rarely occur although lymph node, bone, pleura and liver metastases have been reported.

Dane
Klasyfikacja

Choroba

Kod ORPHA
319325
Kod OMIM
-
Kod ICD10
C64
Kod ICD11
-

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