Erythrokeratoderma ''en cocardes''

Orpha code: 315OMIM code:

Definition

A rare, genetic, epidermal disorder characterized by intermittent (remitting and recurring), annular, polycyclic, target-like (or 'en cocardes') plaques with concentric rings of scaling erythema occurring on the extremities, flexural areas, and trunk. Concurrent erythrokeratoderma variabilis-like scaly plaques are commonly found in other parts of the body.

Disease data
Classification

Disease

Synonyms
Degos genodermatosis "en cocardes"
Degos genodermatosis "en cocardes"
ORPHA code
315
OMIM code
-
ICD10 code
Q82.8
ICD11 code
-

No additional description.

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