Spigelian hernia-cryptorchidism syndrome

Orpha code: 314432OMIM code:

Definition

Spigelian hernia-cryptorchidism syndrome is a rare developmental defect during embryogenesis characterized by a ventral, uni- or bilateral protrusion of extraperitoneal fat, peritoneum and/or intra-abdominal organs through a defect in the spigelian fascia (Spigelian hernia), associated with ipsi- or bilateral undescended testis (usually found within or just beneath the hernial sac) in male neonates. The gubernaculum and/or inguinal canal may be absent.

Disease data
Classification

Malformation syndrome

ORPHA code
314432
OMIM code
-
ICD10 code
K43.6
ICD11 code
-

No additional description.

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