Congenital pancreatic cyst

Orpha code: 313906OMIM code:

Definition

A rare pancreatic disease characterized by a most commonly single, unilocular, thin-walled cystic lesion which may be located anywhere within the pancreas (but is more frequently found in the body and tail) and does not communicate with the pancreatic ductal system. Patients may be asymptomatic or present with signs and symptoms of gastrointestinal or biliary obstruction, or pancreatitis. The condition can be isolated or occur in association with other anomalies (such as von Hippel-Lindau disease or polycystic kidney disease).

Disease data
Classification

Morphological anomaly

Synonyms
Neonatal congenital pancreatic cyst
Noworodkowa wrodzona torbiel trzustki
Prawdziwa wrodzona torbiel trzustki
True congenital pancreatic cyst
ORPHA code
313906
OMIM code
-
ICD10 code
Q45.2
ICD11 code
LB21.Y

No additional description.

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