Congenital pancreatic cyst

Orpha code: 313906OMIM code:

Definicja

A rare pancreatic disease characterized by a most commonly single, unilocular, thin-walled cystic lesion which may be located anywhere within the pancreas (but is more frequently found in the body and tail) and does not communicate with the pancreatic ductal system. Patients may be asymptomatic or present with signs and symptoms of gastrointestinal or biliary obstruction, or pancreatitis. The condition can be isolated or occur in association with other anomalies (such as von Hippel-Lindau disease or polycystic kidney disease).

Disease data
Klasyfikacja

Morphological anomaly

Synonimy
Neonatal congenital pancreatic cyst
Noworodkowa wrodzona torbiel trzustki
Prawdziwa wrodzona torbiel trzustki
True congenital pancreatic cyst
Kod ORPHA
313906
Kod OMIM
-
Kod ICD10
Q45.2
Kod ICD11
LB21.Y

No additional description.

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