Nicolaides-Baraitser syndrome

Orpha code: 3051OMIM code: 601358

Definicja

A rare, genetic, syndromic intellectual disability characterized by short stature, sparse hair, characteristic coarse face, brachydactyly with prominent interphalangeal joints, seizures and intellectual disability. Facial characteristics include triangular shaped face, dense and prominent eyelashes, rounded premaxilla, broad nasal base, thick alae nasi, upturned nasal tip, broad philtrum, thin upper vermilion, thick and everted lower vermilion and wide mouth.

Disease data
Klasyfikacja

Malformation syndrome

Synonimy
Intellectual disability-sparse hair-brachydactyly syndrome
Zespół Nicolaidesa i Baraitsera
Kod ORPHA
3051
Kod OMIM
601358
Kod ICD10
Q87.1
Kod ICD11
-

No additional description.

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