Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare genetic disorder of pyrimidine metabolism characterized by early onset of megaloblastic anemia, global developmental delay, and failure to thrive, associated with massive urinary overexcretion of orotic acid (sometimes with orotic acid crystalluria). Patients without megaloblastic anemia, but with additional manifestations such as epilepsy, have also been reported. Disease data Classification Disease Synonyms Orotidylic decarboxylase deficiency Kwasica orotowa Niedobór dekarboksylazy orotydyny Niedobór syntetazy monofosforanu urydyny Uridine monophosphate synthetase deficiency ORPHA code 30 OMIM code 258900 ICD10 code E79.8 ICD11 code 3A03.0 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl