Ollier disease

Orpha code: 296OMIM code: 166000

Definition

A rare primary bone dysplasia characterized by multiple enchondromas (benign cartilage-forming tumors). The lesions are generally unilateral or asymmetrically distributed. The most common affected site is the appendicular skeleton.

Disease data
Classification

Disease

Synonyms
Dyschondroplasia
Choroba Olliera
Dyschondroplazja
ORPHA code
296
OMIM code
166000
ICD10 code
Q78.4
ICD11 code
2E83.Z

No additional description.

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