Methylmalonic acidemia without homocystinuria

Orpha code: 293355OMIM code:

Definition

Methylmalonic acidemia is an inborn error of vitamin B12 metabolism characterized by gastrointestinal and neurometabolic manifestations resulting from decreased function of the mitochondrial enzyme methylmalonyl-CoA mutase.

Disease data
Classification

Clinical group

Synonyms
Methylmalonic aciduria without homocystinuria
Acyduria metylomalonowa bez homocystynurii
ORPHA code
293355
OMIM code
-
ICD10 code
E71.1
ICD11 code
-

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl