Methylmalonic acidemia without homocystinuria

Orpha code: 293355OMIM code:

Definicja

Methylmalonic acidemia is an inborn error of vitamin B12 metabolism characterized by gastrointestinal and neurometabolic manifestations resulting from decreased function of the mitochondrial enzyme methylmalonyl-CoA mutase.

Disease data
Klasyfikacja

Clinical group

Synonimy
Methylmalonic aciduria without homocystinuria
Acyduria metylomalonowa bez homocystynurii
Kod ORPHA
293355
Kod OMIM
-
Kod ICD10
E71.1
Kod ICD11
-

No additional description.

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