Pleomorphic rhabdomyosarcoma

Orpha code: 293199OMIM code:

Definicja

A rare soft tissue sarcoma characterized by a high-grade lesion occurring almost exclusively in adults, composed of bizarre polygonal, round, and spindle cells with evidence of skeletal muscle differentiation. Patients usually present with a rapidly growing, painful mass located in the deep soft tissues of the extremities, but also other anatomic regions. Prognosis is generally poor.

Disease data
Klasyfikacja

Clinical subtype

Kod ORPHA
293199
Kod OMIM
-
Kod ICD10
C49.9
Kod ICD11
XH4VB5

No additional description.

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