Autoimmune polyendocrinopathy

Orpha code: 282196OMIM code:

Definition

A group of rare endocrine diseases characterized by autoimmune activity against more than one endocrine organ, with possible additional involvement of non-endocrine organs. Autoimmunity is typically directed against different target antigens in different tissues. The two more common autoimmune polyendocrine syndromes (APS), APS type 1 and type 2, have a strong genetic background and have Addison's disease as a major feature. The group furthermore includes APS type 3 and type 4.

Disease data
Classification

Clinical group

Synonyms
APS
APS
Autoimmunologiczny zespół wielogruczołowy
Autoimmune polyglandular syndrome
ORPHA code
282196
OMIM code
-
ICD10 code
E31.0
ICD11 code
5B00

No additional description.

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