Chondrodysplasia with joint dislocations, gPAPP type

Orpha code: 280586OMIM code: 614078

Definicja

A rare, genetic, primary bone dysplasia characterized by prenatal onset of disproportionate short stature, shortening of the limbs, congenital joint dislocations, micrognathia, posterior cleft palate, brachydactyly, short metacarpals and irregular size of the metacarpal epiphyses, supernumerary carpal ossification centers and dysmorphic facial features. In addition, hearing impairment and mild psychomotor delay have also been reported.

Disease data
Klasyfikacja

Malformation syndrome

Synonimy
gPAPP deficiency
Niedobór gPAPP
Kod ORPHA
280586
Kod OMIM
614078
Kod ICD10
M85.0
Kod ICD11
-

No additional description.

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