Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A very rare syndrome characterized by progressive loss of bone, usually the capsal and tarsal bones, resulting in deformity and disability, as well as chronic renal failure in many cases. The bone and renal disorders are sometimes associated with intellectual deficit and facial abnormalities. Disease data Classification Malformation syndrome Synonyms Idiopathic multicentric osteolysis with or without nephropathy Idiopatyczna wielocentryczna osteoliza z lub bez nefropatii ORPHA code 2774 OMIM code 166300 ICD10 code M89.5 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl