Description of the disease * EnglishPolish Pobierz sekcję do PDF Definicja Frontotemporal dementia with motor neuron disease (FTD-MND) is a type of frontotemporal lobar degeneration characterized by the insidious onset (between the ages of 38-78 years) of dementia-associated psychiatric symptoms (e.g. personality changes, uninhibited behavior, irritability, aggressiveness), memory difficulties, global intellectual impairment, emotional disorders and transcortical motor aphasia that eventually leads to mutism, in addition to the manifestations of motor neuron disease such as neurogenic muscular wasting (similar to what is seen in amyotrophic lateral sclerosis; see this term). The disease is progressive, with death occurring 2-5 years after onset. Disease data Klasyfikacja Disease Synonimy FTD-ALS FTD-ALS FTD-MND Otępienie czołowo-skroniowe ze stwardnieniem zanikowym bocznym FTD-MND Frontotemporal dementia with amyotrophic lateral sclerosis Kod ORPHA 275872 Kod OMIM 616439 Kod ICD10 G31.0 Kod ICD11 6D83 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl