Knuckle pads-leukonychia-sensorineural deafness-palmoplantar hyperkeratosis syndrome

Orpha code: 2698OMIM code: 149200

Definicja

A rare, syndromic genetic deafness disease characterized by symmetric or asymmetric knuckle pads (typically located on the distal and interphalangeal joints), leukonychia, diffuse palmoplantar keratoderma, and congenital, mild to moderate sensorineural deafness.

Disease data
Klasyfikacja

Disease

Synonimy
Bart-Pumphrey syndrome
Zespół Barta i Pumphrey'a
Zespół knuckle pads-leukonychia-głuchota czuciowo-nerwowa-hiperkeratoza dłoni i stóp
Knuckle pads-leukonychia-sensorineural deafness-palmoplantar keratoderma syndrome
Knuckle pads-leukonychia-sensorineural hearing loss-palmoplantar hyperkeratosis syndrome
Knuckle pads-leukonychia-sensorineural hearing loss-palmoplantar keratoderma syndrome
Kod ORPHA
2698
Kod OMIM
149200
Kod ICD10
Q82.8
Kod ICD11
LD2H.Y

No additional description.

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