Nephrosis-deafness-urinary tract-digital malformations syndrome

Orpha code: 2669OMIM code: 256200

Definition

A rare, genetic, multiple congenital anomalies syndrome characterized by urinary tract anomalies, nephrosis, conductive deafness, and digital malformations, including short and bifid distal phalanges of thumbs and big toes. There have been no further descriptions in the literature since 1962.

Disease data
Classification

Malformation syndrome

Synonyms
Braun-Bayer syndrome
Zespół Brauna i Bayera
Nephrosis-hearing loss-urinary tract-digital malformations syndrome
ORPHA code
2669
OMIM code
256200
ICD10 code
Q87.8
ICD11 code
LD2H.Y

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl