Fibular aplasia-complex brachydactyly syndrome

Orpha code: 2639OMIM code: 228900

Definition

A rare syndrome characterised by severe reduction or absence of the fibula and complex brachydactyly. Less than 30 cases have been described in the literature so far. The syndrome is inherited in an autosomal recessive manner and is caused by mutations in the cartilage-derived morphogenetic protein-1 gene (<i>GDF5</i>).

Disease data
Classification

Malformation syndrome

Synonyms
Du Pan syndrome
Zespół Du Pan
ORPHA code
2639
OMIM code
228900
ICD10 code
Q73.8
ICD11 code
LD26.0

No additional description.

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