Pyramidal molars-abnormal upper lip syndrome

Orpha code: 2561OMIM code: 200970

Definition

A rare multiple congenital anomalies/dysmorphic syndrome characterized by a variable combination of dental, cutaneous, ocular, and bone abnormalities, including pyramidal and fused molar roots, taurodontism, an abnormal upper lip without a cupid's bow and thickened and wide philtrum, juvenile glaucoma, syndactyly, and clinodactyly. There have been no further descriptions in the literature since 1973.

Disease data
Classification

Malformation syndrome

Synonyms
Ackerman fused molar roots syndrome
Pyramidal molar - jaskra - nieprawidłowa warga górna
ORPHA code
2561
OMIM code
200970
ICD10 code
K00.2
ICD11 code
-

No additional description.

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