Autosomal recessive intermediate Charcot-Marie-Tooth disease type B

Orpha code: 254334OMIM code: 613641

Definicja

An extremely rare subtype of autosomal recessive intermediate Charcot-Marie-Tooth (CMT) disease characterized by a CMT neuropathy associated with developmental delay, self-abusive behavior, dysmorphic features and vestibular Schwannoma. Motor nerve conduction velocities demonstrate features of both demyelinating and axonal pathology.

Disease data
Klasyfikacja

Disease

Synonimy
RI-CMT type B
RI-CMT type B
Kod ORPHA
254334
Kod OMIM
613641
Kod ICD10
G60.0
Kod ICD11
8C20.2

No additional description.

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