Microcephaly-deafness-intellectual disability syndrome

Orpha code: 2533OMIM code: 156620

Definition

Microcephaly-deafness-intellectual disability syndrome is characterised by microcephaly, deafness, intellectual deficit and facial dysmorphism (facial asymmetry, prominent glabella, low-set and cup-shaped ears, protruding lower lip, micrognathia). It has been described in a mother and her son. The mode of inheritance is probably autosomal dominant.

Disease data
Classification

Malformation syndrome

Synonyms
Kawashima-Tsuji syndrome
Zespół Kawashima i Tsuji
Microcephaly-hearing loss-intellectual disability syndrome
ORPHA code
2533
OMIM code
156620
ICD10 code
Q87.8
ICD11 code
LD2H.Y

No additional description.

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