Subependymal giant cell astrocytoma

Orpha code: 251618OMIM code:

Definicja

A rare low-grade astrocytoma characterized by a benign, slowly growing lesion typically arising in the wall of the lateral ventricles, composed of large ganglioid astrocytes. The tumor corresponds to WHO grade I and typically occurs during the first two decades of life in patients with tuberous sclerosis complex. Most patients present with worsening of epilepsy or symptoms of increased intracranial pressure.

Disease data
Klasyfikacja

Disease

Synonimy
SEGA
SEGA
Kod ORPHA
251618
Kod OMIM
-
Kod ICD10
D43.2
Kod ICD11
2A00.0Y

No additional description.

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