Acute neonatal citrullinemia type I

Orpha code: 247546OMIM code:

Definition

A severe form of citrullinemia type 1 characterized biologically by hyperammonemia and clinically by progressive lethargy, poor feeding and vomiting, seizures and possible loss of consciousness, within one to a few days of birth, with variable signs of increased intracranial pressure. The condition can lead to significant neurologic deficits.

Disease data
Classification

Clinical subtype

Synonyms
Acute neonatal citrullinemia type 1
Citrulinemia klasyczna typu 1
Citrulinemia klasyczna typu I
Ostra citrulinemia noworodkowa typu 1
Ostra noworodkowa cytrulinemia typu I
Early-onset citrullinemia type 1
Early-onset citrullinemia type I
ORPHA code
247546
OMIM code
-
ICD10 code
E72.2
ICD11 code
-

No additional description.

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