Laryngo-onycho-cutaneous syndrome

Orpha code: 2407OMIM code: 245660

Definition

LOC syndrome is a subtype of junctional epidermolysis bullosa (JEB, see this term) characterized by an altered cry in the neonatal period and by aberrant production of granulation tissue in particular affecting the upper airway tract, conjunctiva and periungual/subungual sites.

Disease data
Classification

Disease

Synonyms
LOC syndrome
Zespół LOGIC
Zespół Shabbira
Zespół LOC
LOGIC syndrome
Laryngeal and ocular granulation tissue in children from the Indian subcontinent syndrome
Shabbir syndrome
ORPHA code
2407
OMIM code
245660
ICD10 code
Q81.8
ICD11 code
EC31

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl