Papular elastorrhexis

Orpha code: 228264OMIM code:

Definition

A rare, acquired, dermis elastic tissue disorder characterized by multiple, asymptomatic, firm, well-demarcated, nonfollicular, hypopigmented or skin-colored papules, with a diameter of less than 1 cm, distributed symmetrically over trunk and/or proximal limbs (rarely, head, neck, shoulders, armpits, thighs), with no extracutaneous manifestations. Histopathology typically reveals decreased and fragmented elastic fibers, thickened and/or homogenized collagen bundles and, in some, a mild, perivascular, lymphocytic infiltrate in the dermis.

Disease data
Classification

Disease

Synonyms
Eruptive collagenoma Wyrzutowa kolagenoma
Rozsiane znamię ze zwyrodnieniem włókien sprężystych
Znamię ze zwyrodnieniem włókien sprężystych
ORPHA code
228264
OMIM code
-
ICD10 code
L98.8
ICD11 code
EE41.Y

No additional description.

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