Dermatomyositis

Orpha code: 221OMIM code:

Definition

A rare idiopathic inflammatory myopathy (IIM) characterized by evocative skin lesions, muscle involvement with symmetrical proximal muscle weakness, and specific histological features. The clinical subtypes are defined by the presence of myositis-specific antibodies (anti-Mi2, anti-NXP2, anti-TIF1-γ, anti-MDA5, or anti-SAE antibodies) and are associated with specific clinical phenotypes and prognosis.

Disease data
Classification

Disease

Synonyms
Adult dermatomyositis
DM
ORPHA code
221
OMIM code
-
ICD10 code
M33.0
ICD11 code
4A41.00

No additional description.

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