Congenital hydrocephalus

Definition

A rare central nervous system malformation characterized by abnormally enlarged cerebral ventricles due to impaired cerebrospinal fluid circulation. It arises in utero and can be either acquired or inherited. The severity of the resulting brain damage depends on the duration and extent of ventriculomegaly.

Disease data

Classification

Malformation syndrome

ORPHA code

2185

OMIM code

615219

ICD10 code

Q03.0

ICD11 code

LA04

*Soruce