Osteogenesis imperfecta type 4

Orpha code: 216820OMIM code: 616507

Definition

A moderately severe form of osteogenesis imperfecta characterized by increased bone fragility and low bone mass that clinically manifests from infancy as susceptibility to bone fractures, short stature, mild to moderate scoliosis in most, gray-blue or white sclera, and dentinogenesis imperfecta.

Disease data
Classification

Clinical subtype

Synonyms
OI type 4
OI typu 4
ORPHA code
216820
OMIM code
616507
ICD10 code
Q78.0
ICD11 code
LD24.K0

No additional description.

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