Hernández-Aguirre Negrete syndrome

Orpha code: 2139OMIM code:

Definition

A rare multiple congenital anomalies/dysmorphic syndrome characterized by global developmental delay, mild intellectual disability, seizures, obesity, and dysmorphic facial features (including large, bulbous nose, prominent philtrum, wide mouth). Additional reported features are bilateral pes planus, scoliosis, and spina bifida occulta. Brain MRI may show mild ventricular dilatation.

Disease data
Classification

Malformation syndrome

Synonyms
Intellectual disability-epilepsy-bulbous nose syndrome
Niepełnosprawność intelektualna - padaczka - kartoflowaty nos
ORPHA code
2139
OMIM code
-
ICD10 code
Q87.8
ICD11 code
-

No additional description.

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