Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Cryopyrin associated periodic syndrome (CAPS) defines a group of autoinflammatory diseases, characterized by recurrent episodes of systemic inflammatory attacks in the absence of infection or autoimmune disease. CAPS comprises 3 disorders on a continuum of severity: severe CINCA syndrome, intermediate Muckle-Wells syndrome (MWS) and milder familial cold urticaria (FCAS) (see these terms). Disease data Classification Clinical group Synonyms CAPS CAPS Kriopirynopatia Cryopyrinopathy NLRP3-associated systemic autoinflammatory disease ORPHA code 208650 OMIM code - ICD10 code E85.0 ICD11 code 4A60.1 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl