Gamma-aminobutyric acid transaminase deficiency

Orpha code: 2066OMIM code: 613163

Definition

A rare disorder of gamma-aminobutyric acid (GABA) metabolism characterized by a severe neonatal-infantile epileptic encephalopathy (manifesting with symptoms such as seizures, hypotonia, hyperreflexia and developmental delay) and growth acceleration.

Disease data
Classification

Disease

Synonyms
GABA transaminase deficiency
Niedobór transaminazy GABA
ORPHA code
2066
OMIM code
613163
ICD10 code
E72.8
ICD11 code
5C59.1

No additional description.

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