Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare form of idiopathic inflammatory myopathy characterized by acute or subacute, severe, symmetrical, proximal muscle weakness usually associated with muscle-specific antibodies (anti-HMGCR or anti-SRP). Histopathological characteristics include myocyte necrosis and regeneration without significant inflammation, and C5b-9 deposition on non-necrotic myofibers. Disease data Classification Disease Synonyms Anti-HMG-CoA myopathy NAM IMNM Miopatia anty-SRP Miopatia anty-HMG-CoA Autoimmunologiczne martwicze zapalenie mięsni Miopatia immunologiczna z martwicą miocytów Anti-SRP myopathy Autoimmune necrotizing myositis IMNM Immune myopathy with myocyte necrosis NAM ORPHA code 206569 OMIM code - ICD10 code G72.4 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl