Hypoxanthine-guanine phosphoribosyltransferase deficiency

Orpha code: 206428OMIM code:

Definition

Hypoxanthine-guanine phosphoribosyltransferase (HPRT) deficiency is a hereditary disorder of purine metabolism associated with uric acid overproduction and a continuum spectrum of neurological manifestations depending on the degree of the enzyme deficiency.

Disease data
Classification

Clinical group

Synonyms
HPRT deficiency
Niedobór fosforybozyltransferazy hipoksantynowo-guaninowej 1
Niedobór HPRT deficiency
Niedobór HPRT1
HPRT1 deficiency
Hypoxanthine-guanine phosphoribosyltransferase 1 deficiency
ORPHA code
206428
OMIM code
-
ICD10 code
E79.8
ICD11 code
-

No additional description.

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