Alar cartilages hypoplasia-coloboma-telecanthus syndrome

Orpha code: 2007OMIM code: 203000

Definition

A very rare dysmorphic disorder characterized by hypoplasia and coloboma of the alar cartilages and telecanthus described in 2 sisters. No new cases with similar features have been reported since 1976.

Disease data
Classification

Malformation syndrome

ORPHA code
2007
OMIM code
203000
ICD10 code
Q75.8
ICD11 code
-

No additional description.

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