Cleft lip/palate-intestinal malrotation-cardiopathy syndrome

Orpha code: 2001OMIM code: 601165

Definition

A rare multiple congenital anomaly syndrome characterized by flat face, hypertelorism, flat occiput, upward slanting palpebral fissures, cleft palate, micrognathia, short neck, and severe congenital heart defects. Malrotation of the intestine, bilateral clinodactyly, bilobed tongue, short fourth metatarsals and bifid thumbs may be additionally observed.

Disease data
Classification

Malformation syndrome

Synonyms
McPherson-Clemens syndrome
Zespół McPhersona i Clemensa
ORPHA code
2001
OMIM code
601165
ICD10 code
Q87.8
ICD11 code
-

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl