Calcifying aponeurotic fibroma

Orpha code: 199260OMIM code:

Definition

A rare, superficial fibromatosis characterized by non-malignant, locally invading, fibrosing tumour of differentiated fibroblasts, slowly growing subcutaneously, occurring predominantly distally on the extremities, especially the hands and feet. Histologic examination shows a multinodular pattern with large areas of calcification and fibrosis, and the presence of elongated spindle cells with hyperchromatic plump vesicular nuclei interspersed within fine bands of collagen.

Disease data
Classification

Disease

Synonyms
Juvenile aponeurotic fibromatosis
Guz Keasby'ego
Młodzieńcza włókniakowatość rozcięgna
Keasby tumor
ORPHA code
199260
OMIM code
-
ICD10 code
M72.8
ICD11 code
EE61

No additional description.

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