Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare, superficial fibromatosis characterized by non-malignant, locally invading, fibrosing tumour of differentiated fibroblasts, slowly growing subcutaneously, occurring predominantly distally on the extremities, especially the hands and feet. Histologic examination shows a multinodular pattern with large areas of calcification and fibrosis, and the presence of elongated spindle cells with hyperchromatic plump vesicular nuclei interspersed within fine bands of collagen. Disease data Classification Disease Synonyms Juvenile aponeurotic fibromatosis Guz Keasby'ego Młodzieńcza włókniakowatość rozcięgna Keasby tumor ORPHA code 199260 OMIM code - ICD10 code M72.8 ICD11 code EE61 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl