Corticosteroid-binding globulin deficiency

Orpha code: 199247OMIM code: 611489

Definicja

Corticosteroid-binding globulin deficiency is a rare, genetic, adrenal disease characterized by diminished corticosteroid-binding capacity associated with normal or low plasma corticosteroid-binding globulin concentration and reduced total plasma cortisol levels. Patients typically present chronic pain, fatigue and hypo/hypertension.

Disease data
Klasyfikacja

Disease

Synonimy
Transcortin deficiency
Niedobór transkortyny
Kod ORPHA
199247
Kod OMIM
611489
Kod ICD10
E27.8
Kod ICD11
-

No additional description.

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