Progressive cone dystrophy

Orpha code: 1871OMIM code: 613093

Definition

A rare retinal dystrophy characterized by photophobia, progressive loss of visual acuity, nystagmus, visual field abnormalities, abnormal color vision, and psychophysical and electrophysiological evidence of abnormal cone function. Progressive cone dystrophy usually presents in childhood or early adult life, and patients tend to develop rod photoreceptor dysfunction in later life.

Disease data
Classification

Disease

Synonyms
Cone dystrophy
Dystrofia stożka
ORPHA code
1871
OMIM code
613093
ICD10 code
H35.5
ICD11 code
9B70

No additional description.

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