Bleeding disorder in hemophilia B carriers

Orpha code: 177929OMIM code: 306900

Definition

A rare bleeding disorder in association with carrier mutations in the <i>F9</i> gene (Xq27.1) encoding coagulation factor IX (FIX), with a biological activity of FIX &#8805;40 IU/dL and characterized clinically by abnormal bleeding as a result of minor injuries or following trauma, surgery or tooth extraction. Spontaneous hemorrhages may occur occasionally. Heavy menstrual bleeding is the most frequent type of bleed in the carriers.

Disease data
Classification

Clinical subtype

Synonyms
Krwawienie u nosicieli hemofilii B
ORPHA code
177929
OMIM code
306900
ICD10 code
D67
ICD11 code
-

No additional description.

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