Bleeding disorder in hemophilia A carriers

Orpha code: 177926OMIM code: 306700

Definition

A rare bleeding disorder in association with carrier mutations in the <i>F8</i> gene (Xq28) encoding coagulation factor VIII (FVIII), with a biological activity of FVIII &#8805;40 IU/dL and characterized clinically by abnormal bleeding as a result of minor injuries or following trauma, surgery or tooth extraction. Spontaneous hemorrhages may occur occasionally. Heavy menstrual bleeding is the most frequent type of bleed in the carriers.

Disease data
Classification

Clinical subtype

Synonyms
Krwawienie u nosicieli hemofilii A
ORPHA code
177926
OMIM code
306700
ICD10 code
D66
ICD11 code
-

No additional description.

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