Bleeding disorder in hemophilia A carriers

Orpha code: 177926OMIM code: 306700

Definicja

A rare bleeding disorder in association with carrier mutations in the <i>F8</i> gene (Xq28) encoding coagulation factor VIII (FVIII), with a biological activity of FVIII &#8805;40 IU/dL and characterized clinically by abnormal bleeding as a result of minor injuries or following trauma, surgery or tooth extraction. Spontaneous hemorrhages may occur occasionally. Heavy menstrual bleeding is the most frequent type of bleed in the carriers.

Disease data
Klasyfikacja

Clinical subtype

Synonimy
Krwawienie u nosicieli hemofilii A
Kod ORPHA
177926
Kod OMIM
306700
Kod ICD10
D66
Kod ICD11
-

No additional description.

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