Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A severe form of hemophilia A characterized by a large deficiency of factor VIII (biological activity <1 IU/dL) leading to frequent spontaneous hemorrhage and abnormal bleeding as a result of minor injuries, or following trauma, surgery or tooth extraction. It primarily affects males but may also be observed in female carriers of disease-causing mutations. Disease data Classification Clinical subtype Synonyms Severe congenital F8 deficiency Ciężki Niedobór czynnika VIII Severe congenital factor VIII deficiency ORPHA code 169802 OMIM code 306700 ICD10 code D66 ICD11 code 3B10.0 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl