Severe hemophilia B

Orpha code: 169793OMIM code: 306900

Definicja

A severe form of hemophilia B characterized by a large deficiency of factor IX (biological activity <1 IU/dL) leading to frequent spontaneous hemorrhage and abnormal bleeding as a result of minor injuries or following trauma, surgery or tooth extraction. It primarily affects males but may also be observed in female carriers of disease-causing mutations.

Disease data
Klasyfikacja

Clinical subtype

Synonimy
Severe congenital F9 deficiency
Ciężki Niedobór czynnika IX
Severe congenital factor IX deficiency
Kod ORPHA
169793
Kod OMIM
306900
Kod ICD10
D67
Kod ICD11
3B11.0

No additional description.

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