Spondylometaphyseal dysplasia, Golden type

Orpha code: 168544OMIM code: 313420

Definicja

Spondylometaphyseal dysplasia, Golden type is a rare primary bone dysplasia disorder characterized by severe short stature, coarse facies, thoracolumbar kyphoscoliosis and enlarged joints with contractures. Psychomotor delay and intellectual disability may also be associated. Radiographic features include flat vertebral bodies, lacy ossification of the metaphyses of long bones and iliac crests, and marked sclerosis of the skull base.

Disease data
Klasyfikacja

Disease

Synonimy
X-linked spondylometaphyseal dysplasia
Dysplazja kręgowo-przynasadowa sprzężona z chromosomem X
Kod ORPHA
168544
Kod OMIM
313420
Kod ICD10
Q77.8
Kod ICD11
LD24.4

No additional description.

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