Split cord malformation type I

Orpha code: 1671OMIM code: 222500

Definition

A rare subtype of split cord malformation characterized by each hemicord contained in its own dural sac, typically with a intervening bony septum.

Disease data
Classification

Morphological anomaly

Synonyms
SCM type 1
SCM type I
Split cord malformation type 1
Diastematomyelia
ORPHA code
1671
OMIM code
222500
ICD10 code
Q06.2
ICD11 code
LA07.1

No additional description.

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